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Medications for Cystic Fibrosis

About Cystic Fibrosis:  Cystic fibrosis is an inherited disease that affects sodium channels in the body and causes respiratory and digestive problems.

See also: sub-topics

Drugs Used to Treat Cystic Fibrosis

The following list of medications are in some way related to, or used in the treatment of this condition.

Drug name Rx / OTC Pregnancy CSA Alcohol Reviews Rating Popularity
Pulmozyme B N 1 review
10

Generic name: dornase alfa systemic

Drug class: miscellaneous respiratory agents

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Creon C N 4 reviews
10

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

azithromycin B N 1 review
9.0

Generic name: azithromycin systemic

Brand names:  Zithromax, Azithromycin Dose Pack, Zmax

Drug class: macrolides

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Prescribing Information

tobramycin D N Add review
9.0

Generic name: tobramycin systemic

Brand names:  Tobi, TOBI Podhaler, Bethkis, Kitabis Pak …show all

Drug class: aminoglycosides, inhaled anti-infectives

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Prescribing Information

Kalydeco B N 1 review
10

Generic name: ivacaftor systemic

Drug class: CFTR potentiators

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

dornase alfa B N 1 review
10

Generic name: dornase alfa systemic

Brand name:  Pulmozyme

Drug class: miscellaneous respiratory agents

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph

Cayston B N Add review
10

Generic name: aztreonam systemic

Drug class: miscellaneous antibiotics

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

pancrelipase C N 5 reviews
9.0

Generic name: pancrelipase systemic

Brand names:  Creon, Zenpep, Pancreaze, Viokase, Pertzye, Ultresa, Pangestyme EC, Panocaps, Viokace …show all

Drug class: digestive enzymes

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Prescribing Information

Tobi D N Add review
9.0

Generic name: tobramycin systemic

Drug class: aminoglycosides, inhaled anti-infectives

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Zenpep C N Add review
9.0

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

vitamin e C N Add review Rate

Generic name: vitamin e systemic

Brand names:  Alpha E, Aqua-E, Aqua Gem-E, Aquasol E, Aquavite-E, E Pherol, Nutr-E-Sol, Vita-Plus E Natural, E-400 Clear, E-600, E-Gems …show all

Drug class: vitamins

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Natural Product Monographs

Zithromax B N 1 review
9.0

Generic name: azithromycin systemic

Drug class: macrolides

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

ivacaftor B N 1 review
10

Generic name: ivacaftor systemic

Brand name:  Kalydeco

Drug class: CFTR potentiators

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph

Amikin D N 1 review
1.0

Generic name: amikacin systemic

Drug class: aminoglycosides

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Orkambi B N Add review Rate

Generic name: ivacaftor / lumacaftor systemic

Drug class: CFTR combinations

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Azithromycin Dose Pack B N Add review Rate

Generic name: azithromycin systemic

Drug class: macrolides

For consumers: dosage, interactions, side effects

aztreonam B N Add review
10

Generic name: aztreonam systemic

Brand names:  Cayston, Azactam

Drug class: miscellaneous antibiotics

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Prescribing Information

amikacin D N 1 review
1.0

Generic name: amikacin systemic

Brand names:  Amikin, Amikin Pediatric

Drug class: aminoglycosides

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Prescribing Information

Pancreaze C N Add review Rate

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Garamycin D N Add review Rate

Generic name: gentamicin systemic

Drug class: aminoglycosides

For consumers: dosage, interactions, side effects

gentamicin D N Add review Rate

Generic name: gentamicin systemic

Brand name:  Garamycin

Drug class: aminoglycosides

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph, Prescribing Information

TOBI Podhaler D N Add review Rate

Generic name: tobramycin systemic

Drug class: aminoglycosides, inhaled anti-infectives

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

ivacaftor / lumacaftor B N Add review Rate

Generic name: ivacaftor / lumacaftor systemic

Brand name:  Orkambi

Drug class: CFTR combinations

For consumers: dosage, interactions,

For professionals: A-Z Drug Facts, AHFS DI Monograph

Zmax B N Add review Rate

Generic name: azithromycin systemic

Drug class: macrolides

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Viokase C N Add review Rate

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

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Topics under Cystic Fibrosis

Learn more about Cystic Fibrosis

Micromedex® Care Notes

Symptoms and treatments

Mayo Clinic Reference

Legend

Off Label This medication may not be approved by the FDA for the treatment of this condition.
Prescription Only / Over the Counter
Rx Prescription Only
OTC Over the Counter
Rx/OTC Prescription or Over the Counter
Pregnancy
A Adequate and well-controlled studies have failed to demonstrate a risk to the fetus in the first trimester of pregnancy (and there is no evidence of risk in later trimesters).
B Animal reproduction studies have failed to demonstrate a risk to the fetus and there are no adequate and well-controlled studies in pregnant women.
C Animal reproduction studies have shown an adverse effect on the fetus and there are no adequate and well-controlled studies in humans, but potential benefits may warrant use in pregnant women despite potential risks.
D There is positive evidence of human fetal risk based on adverse reaction data from investigational or marketing experience or studies in humans, but potential benefits may warrant use in pregnant women despite potential risks.
X Studies in animals or humans have demonstrated fetal abnormalities and/or there is positive evidence of human fetal risk based on adverse reaction data from investigational or marketing experience, and the risks involved in use in pregnant women clearly outweigh potential benefits.
N FDA has not classified the drug.
Controlled Substances Act Schedule
N Is not subject to the Controlled Substances Act.
1 Has a high potential for abuse. Has no currently accepted medical use in treatment in the United States. There is a lack of accepted safety for use under medical supervision.
2 Has a high potential for abuse. Has a currently accepted medical use in treatment in the United States or a currently accepted medical use with severe restrictions. Abuse may lead to severe psychological or physical dependence.
3 Has a potential for abuse less than those in schedules 1 and 2. Has a currently accepted medical use in treatment in the United States. Abuse may lead to moderate or low physical dependence or high psychological dependence.
4 Has a low potential for abuse relative to those in schedule 3. It has a currently accepted medical use in treatment in the United States. Abuse may lead to limited physical dependence or psychological dependence relative to those in schedule 3.
5 Has a low potential for abuse relative to those in schedule 4. Has a currently accepted medical use in treatment in the United States. Abuse may lead to limited physical dependence or psychological dependence relative to those in schedule 4.
Alcohol
X Interacts with Alcohol.

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