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Medications for Cystic Fibrosis

Cystic fibrosis is an inherited disease that affects sodium channels in the body and causes respiratory and digestive problems.

Drugs used to treat Cystic Fibrosis

The following list of medications are in some way related to or used in the treatment of this condition.

Drug name Rating Reviews Activity ? Rx/OTC Pregnancy CSA Alcohol
Pulmozyme 10 1 review
Rx B N

Generic name: dornase alfa systemic

Drug class: miscellaneous respiratory agents

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Creon 8.2 5 reviews
Rx C N

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

azithromycin 9.0 1 review
Rx B N

Generic name: azithromycin systemic

Brand names:  Zithromax, Azithromycin Dose Pack

Drug class: macrolides

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Kalydeco 10 1 review
Rx B N

Generic name: ivacaftor systemic

Drug class: CFTR potentiators

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

tobramycin Rate Add review
Rx D N

Generic name: tobramycin systemic

Brand names:  Tobi, TOBI Podhaler, Bethkis, Kitabis Pak …show all

Drug class: aminoglycosides, inhaled anti-infectives

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Cayston Rate Add review
Rx B N

Generic name: aztreonam systemic

Drug class: miscellaneous antibiotics

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

dornase alfa 10 1 review
Rx B N

Generic name: dornase alfa systemic

Brand name:  Pulmozyme

Drug class: miscellaneous respiratory agents

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph

vitamin e Rate Add review
Rx/OTC C N

Generic name: vitamin e systemic

Brand names:  Alpha E, Aqua Gem-E, Aquasol E, E-400 Clear, E-600, E-Gems, E Pherol …show all

Drug class: vitamins

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Natural Product Monographs

Orkambi Rate Add review
Rx B N

Generic name: ivacaftor / lumacaftor systemic

Drug class: CFTR combinations

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Symdeko Rate Add review
Rx N

Generic name: ivacaftor / tezacaftor systemic

Drug class: CFTR combinations

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Tobi Rate Add review
Rx D N

Generic name: tobramycin systemic

Drug class: aminoglycosides, inhaled anti-infectives

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Zenpep 10 1 review
Rx C N

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

pancrelipase 8.5 8 reviews
Rx/OTC C N

Generic name: pancrelipase systemic

Brand names:  Creon, Zenpep, Pancreaze, Pertzye, Viokace …show all

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Trikafta 9.0 1 review
Rx N

Generic name: elexacaftor / ivacaftor / tezacaftor systemic

Drug class: CFTR combinations

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

Zithromax 9.0 1 review
Rx B N

Generic name: azithromycin systemic

Drug class: macrolides

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

ivacaftor 10 1 review
Rx B N

Generic name: ivacaftor systemic

Brand name:  Kalydeco

Drug class: CFTR potentiators

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph

amikacin 1.0 1 review
Rx D N

Generic name: amikacin systemic

Brand names:  Amikin, Amikin Pediatric

Drug class: aminoglycosides

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Azithromycin Dose Pack Rate Add review
Rx B N

Generic name: azithromycin systemic

Drug class: macrolides

For consumers: dosage, interactions, side effects

Amikin 1.0 1 review
Rx D N

Generic name: amikacin systemic

Drug class: aminoglycosides

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

aztreonam Rate Add review
Rx B N

Generic name: aztreonam systemic

Brand names:  Cayston, Azactam

Drug class: miscellaneous antibiotics

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Garamycin Rate Add review
Rx D N

Generic name: gentamicin systemic

Drug class: aminoglycosides

For consumers: dosage, interactions, side effects

TOBI Podhaler Rate Add review
Rx D N

Generic name: tobramycin systemic

Drug class: aminoglycosides, inhaled anti-infectives

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

gentamicin Rate Add review
Rx D N

Generic name: gentamicin systemic

Brand name:  Garamycin

Drug class: aminoglycosides

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph, Prescribing Information

Pancreaze Rate Add review
Rx C N

Generic name: pancrelipase systemic

Drug class: digestive enzymes

For consumers: dosage, interactions, side effects

For professionals: Prescribing Information

ivacaftor / lumacaftor Rate Add review
Rx B N

Generic name: ivacaftor / lumacaftor systemic

Brand name:  Orkambi

Drug class: CFTR combinations

For consumers: dosage, interactions, side effects

For professionals: AHFS DI Monograph

Learn more about Cystic Fibrosis

Care guides

Symptoms and treatments

Legend

Rating For ratings, users were asked how effective they found the medicine while considering positive/adverse effects and ease of use (1 = not effective, 10 = most effective).
Activity Activity is based on recent site visitor activity relative to other medications in the list.
Rx Prescription only.
OTC Over-the-counter.
Rx/OTC Prescription or Over-the-counter.
Off-label This medication may not be approved by the FDA for the treatment of this condition.
EUA An Emergency Use Authorization (EUA) allows the FDA to authorize unapproved medical products or unapproved uses of approved medical products to be used in a declared public health emergency when there are no adequate, approved, and available alternatives.
Pregnancy Category
A Adequate and well-controlled studies have failed to demonstrate a risk to the fetus in the first trimester of pregnancy (and there is no evidence of risk in later trimesters).
B Animal reproduction studies have failed to demonstrate a risk to the fetus and there are no adequate and well-controlled studies in pregnant women.
C Animal reproduction studies have shown an adverse effect on the fetus and there are no adequate and well-controlled studies in humans, but potential benefits may warrant use in pregnant women despite potential risks.
D There is positive evidence of human fetal risk based on adverse reaction data from investigational or marketing experience or studies in humans, but potential benefits may warrant use in pregnant women despite potential risks.
X Studies in animals or humans have demonstrated fetal abnormalities and/or there is positive evidence of human fetal risk based on adverse reaction data from investigational or marketing experience, and the risks involved in use in pregnant women clearly outweigh potential benefits.
N FDA has not classified the drug.
Controlled Substances Act (CSA) Schedule
M The drug has multiple schedules. The schedule may depend on the exact dosage form or strength of the medication.
U CSA Schedule is unknown.
N Is not subject to the Controlled Substances Act.
1 Has a high potential for abuse. Has no currently accepted medical use in treatment in the United States. There is a lack of accepted safety for use under medical supervision.
2 Has a high potential for abuse. Has a currently accepted medical use in treatment in the United States or a currently accepted medical use with severe restrictions. Abuse may lead to severe psychological or physical dependence.
3 Has a potential for abuse less than those in schedules 1 and 2. Has a currently accepted medical use in treatment in the United States. Abuse may lead to moderate or low physical dependence or high psychological dependence.
4 Has a low potential for abuse relative to those in schedule 3. It has a currently accepted medical use in treatment in the United States. Abuse may lead to limited physical dependence or psychological dependence relative to those in schedule 3.
5 Has a low potential for abuse relative to those in schedule 4. Has a currently accepted medical use in treatment in the United States. Abuse may lead to limited physical dependence or psychological dependence relative to those in schedule 4.
Alcohol
X Interacts with Alcohol.

Further information

Always consult your healthcare provider to ensure the information displayed on this page applies to your personal circumstances.

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