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Cysteamine Dosage

Medically reviewed by Drugs.com. Last updated on Mar 14, 2023.

Applies to the following strengths: 50 mg; 150 mg; 25 mg; 75 mg; 300 mg

Usual Adult Dose for Nephropathic Cystinosis

Immediate-release capsule:
Less than 110 lbs: Data not available
110 lbs or more:


Delayed-release capsule:

Comments:

Use: Management of nephropathic cystinosis

Usual Pediatric Dose for Nephropathic Cystinosis

Immediate-release capsule:
Less than 12 years old:


12 years or older:
Less than 110 lbs: Data not available
110 lbs or more:

Delayed-release capsule:
Less than 6 years: Safety has not been established.
6 years and older:

Comments:

Use: Management of nephropathic cystinosis

Renal Dose Adjustments

Data not available

Liver Dose Adjustments

Data not available

Dose Adjustments

Transferring patients from immediate-release to delayed-release capsules:


Transferring from cysteamine hydrochloride or phosphocysteamine solutions:

To achieve the target WBC cystine concentration (or plasma cysteamine concentration) or in case of intolerance: Increase or decrease dose by 10%, up to maximum daily dose of 1.95 g/m2.

Titration based on WBC Cystine:

Titration based on plasma cysteamine:

Monitor WBC cysteine levels or plasma cysteamine concentration:

Precautions

Safety and efficacy for the delayed-release capsules have not been established in patients younger than 6 years.

Consult WARNINGS section for additional precautions.

Dialysis

Cysteamine is dialyzable; however, no dose adjustment guidelines have been reported.

Other Comments

Administration advice:


Missed dose:

Delayed-release administration options:

General:

Monitoring:
Hematologic:

Patient advice:

Further information

Always consult your healthcare provider to ensure the information displayed on this page applies to your personal circumstances.