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Pulmonary Fibrosis

WHAT YOU NEED TO KNOW:

What is pulmonary fibrosis?

Pulmonary fibrosis is the scarring of your lung tissues over time. It is also called interstitial lung disease. The air sacs and tissues in your lungs swell, scars form, and the tissues become thick and stiff. This affects how much oxygen you get and makes it hard to breathe.

What increases my risk for pulmonary fibrosis?

The cause of pulmonary fibrosis may not be known. The following may increase your risk:

  • Family history of pulmonary fibrosis or other lung disease
  • Chemicals, such as asbestos, silica, or pesticides
  • Tobacco smoke
  • Medical conditions, such as acid reflux, arthritis, or diabetes
  • Medicines, such as antibiotics and antidepressants
  • Treatment for medical conditions, such as radiation

What are the signs and symptoms of pulmonary fibrosis?

  • Trouble breathing that gets worse over time
  • Dry cough
  • Fast heartbeat
  • Clubbing of fingertips and nails (become large, blunt, and rounded)
  • Tiredness and weakness

How is pulmonary fibrosis treated?

There is no cure for pulmonary fibrosis. The goal of treatment is to slow the progress of the disease and treat your symptoms. You may need any of the following:

  • Extra oxygen may be needed if your blood oxygen level is lower than it should be. You may get oxygen through a mask placed over your nose and mouth or through small tubes placed in your nostrils.
  • Medicines may be given to decrease lung tissue swelling and help prevent scarring.
  • Surgery may be needed if you have severe trouble breathing. You may need part of your lung removed or a lung transplant.

How can I manage my symptoms?

  • Use oxygen at home as directed. Oxygen is usually given through a nasal cannula. This is a pair of short, thin tubes that rest just inside your nose. Tell your healthcare provider if your nose gets dry or if the skin gets red or sore. Never smoke or let anyone else smoke in the same room while your oxygen is on.
  • Do breathing exercises to help you breathe more easily. Breathe out with pursed or puckered lips. Use your diaphragm to breathe. Put one hand on your abdomen and breathe in, causing your hand to move outward or upward. This helps make more room so your lungs can take in more air.
  • Go to pulmonary rehab as directed. Specialists will help you safely strengthen your lungs and prevent more tissue damage. The plan includes education about your condition, exercise, breathing strategies, and ways to conserve energy. Pulmonary rehab may help decrease your breathing problems and help you function better in your daily activities.
  • Get the flu vaccine every year as soon as it becomes available. You may also need the pneumococcal vaccine to prevent pneumonia.
  • Do not smoke. Nicotine and other chemicals in cigarettes and cigars can increase the damage to your lung tissue. Ask your healthcare provider for information if you currently smoke and need help to quit. E-cigarettes or smokeless tobacco still contain nicotine. Talk to your healthcare provider before you use these products.

Where can I find more information?

  • American Lung Association
    1301 Pennsylvania Ave. NW
    Washington , DC 20004
    Phone: 1- 202 - 785-3355
    Phone: 1- 800 - 548-8252
    Web Address: www.lung.org
  • Pulmonary Fibrosis Foundation
    230 East Ohio Street
    Chicago , IL 60611-3201
    Phone: 1- 888 - 733-6741
    Web Address: www.pulmonaryfibrosis.org

Call your local emergency number (911 in the US) if:

  • You have sudden severe trouble breathing.
  • You have a fast heartbeat or chest pain.
  • Your shortness of breath gets worse.
  • You feel so dizzy that you cannot stand up.

When should I call my doctor?

  • You have a fever.
  • You cough up bloody mucus.
  • You are wheezing.
  • Your lips or fingernails turn blue.
  • You have swelling in your legs or feet.
  • You need more oxygen than you used to.
  • You have questions or concerns about your condition or care.

Care Agreement

You have the right to help plan your care. Learn about your health condition and how it may be treated. Discuss treatment options with your healthcare providers to decide what care you want to receive. You always have the right to refuse treatment. The above information is an educational aid only. It is not intended as medical advice for individual conditions or treatments. Talk to your doctor, nurse or pharmacist before following any medical regimen to see if it is safe and effective for you.

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Further information

Always consult your healthcare provider to ensure the information displayed on this page applies to your personal circumstances.

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