Skip to main content

Medications for Cystic Fibrosis

Cystic fibrosis is an inherited disease that affects sodium channels in the body and causes respiratory and digestive problems.

Drugs used to treat Cystic Fibrosis

The following list of medications are in some way related to or used in the treatment of this condition.

Filter
Drug name Rating Reviews Activity ? Rx/OTC Pregnancy CSA Alcohol
Pulmozyme 10 1 review for Pulmozyme to treat Cystic Fibrosis
Rx B N
Generic name:
dornase alfa systemic
Drug class:
miscellaneous respiratory agents
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Creon 8.2 5 reviews for Creon to treat Cystic Fibrosis
Rx C N
Generic name:
pancrelipase systemic
Drug class:
digestive enzymes
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
azithromycin 9.0 1 review for azithromycin to treat Cystic Fibrosis
Rx B N
Generic name:
azithromycin systemic
Brand names:
Zithromax, Azithromycin Dose Pack
Drug class:
macrolides
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Prescribing Information
Kalydeco 10 1 review for Kalydeco to treat Cystic Fibrosis
Rx B N
Generic name:
ivacaftor systemic
Drug class:
CFTR potentiators
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Trikafta 9.0 1 review for Trikafta to treat Cystic Fibrosis
Rx N
Generic name:
elexacaftor / ivacaftor / tezacaftor systemic
Drug class:
CFTR combinations
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
tobramycin Rate Add review
Rx D N
Generic name:
tobramycin systemic
Brand names:
Tobi, TOBI Podhaler, Bethkis, Kitabis Pak
Drug class:
aminoglycosides, inhaled anti-infectives
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Prescribing Information
Cayston Rate Add review
Rx B N
Generic name:
aztreonam systemic
Drug class:
miscellaneous antibiotics
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
dornase alfa 10 1 review for dornase alfa to treat Cystic Fibrosis
Rx B N
Generic name:
dornase alfa systemic
Brand name:
Pulmozyme
Drug class:
miscellaneous respiratory agents
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph
vitamin e Rate Add review
Rx/OTC C N
Generic name:
vitamin e systemic
Brand names:
Alpha E, Aqua Gem-E, Aquasol E, E-400 Clear, E-600, E-Gems, E Pherol
Drug class:
vitamins
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Natural Product Monographs
Zenpep 10 1 review for Zenpep to treat Cystic Fibrosis
Rx C N
Generic name:
pancrelipase systemic
Drug class:
digestive enzymes
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Symdeko Rate Add review
Rx N
Generic name:
ivacaftor / tezacaftor systemic
Drug class:
CFTR combinations
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Tobi Rate Add review
Rx D N
Generic name:
tobramycin systemic
Drug class:
aminoglycosides, inhaled anti-infectives
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Orkambi Rate Add review
Rx B N
Generic name:
ivacaftor / lumacaftor systemic
Drug class:
CFTR combinations
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
pancrelipase 8.5 8 reviews for pancrelipase to treat Cystic Fibrosis
Rx/OTC C N
Generic name:
pancrelipase systemic
Brand names:
Creon, Zenpep, Pancreaze, Pertzye, Viokace
Drug class:
digestive enzymes
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Prescribing Information
Zithromax 9.0 1 review for Zithromax to treat Cystic Fibrosis
Rx B N
Generic name:
azithromycin systemic
Drug class:
macrolides
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Azithromycin Dose Pack Rate Add review
Rx B N
Generic name:
azithromycin systemic
Drug class:
macrolides
For consumers:
dosage, interactions, side effects
ivacaftor 10 1 review for ivacaftor to treat Cystic Fibrosis
Rx B N
Generic name:
ivacaftor systemic
Brand name:
Kalydeco
Drug class:
CFTR potentiators
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph
amikacin 1.0 1 review for amikacin to treat Cystic Fibrosis
Rx D N
Generic name:
amikacin systemic
Brand names:
Amikin, Amikin Pediatric
Drug class:
aminoglycosides
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Prescribing Information
TOBI Podhaler Rate Add review
Rx D N
Generic name:
tobramycin systemic
Drug class:
aminoglycosides, inhaled anti-infectives
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Amikin 1.0 1 review for Amikin to treat Cystic Fibrosis
Rx D N
Generic name:
amikacin systemic
Drug class:
aminoglycosides
For consumers:
dosage, interactions, side effects
aztreonam Rate Add review
Rx B N
Generic name:
aztreonam systemic
Brand names:
Cayston, Azactam
Drug class:
miscellaneous antibiotics
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Prescribing Information
Pancreaze Rate Add review
Rx C N
Generic name:
pancrelipase systemic
Drug class:
digestive enzymes
For consumers:
dosage, interactions, side effects
For professionals:
Prescribing Information
Garamycin Rate Add review
Rx D N
Generic name:
gentamicin systemic
Drug class:
aminoglycosides
For consumers:
dosage, interactions, side effects
gentamicin Rate Add review
Rx D N
Generic name:
gentamicin systemic
Brand name:
Garamycin
Drug class:
aminoglycosides
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph, Prescribing Information
ivacaftor / lumacaftor Rate Add review
Rx B N
Generic name:
ivacaftor / lumacaftor systemic
Brand name:
Orkambi
Drug class:
CFTR combinations
For consumers:
dosage, interactions, side effects
For professionals:
AHFS DI Monograph

Frequently asked questions

View more FAQ

Learn more about Cystic Fibrosis

Care guides

Symptoms and treatments

Legend

Rating For ratings, users were asked how effective they found the medicine while considering positive/adverse effects and ease of use (1 = not effective, 10 = most effective).
Activity Activity is based on recent site visitor activity relative to other medications in the list.
Rx Prescription only.
OTC Over-the-counter.
Rx/OTC Prescription or Over-the-counter.
Off-label This medication may not be approved by the FDA for the treatment of this condition.
EUA An Emergency Use Authorization (EUA) allows the FDA to authorize unapproved medical products or unapproved uses of approved medical products to be used in a declared public health emergency when there are no adequate, approved, and available alternatives.
Expanded Access Expanded Access is a potential pathway for a patient with a serious or immediately life-threatening disease or condition to gain access to an investigational medical product (drug, biologic, or medical device) for treatment outside of clinical trials when no comparable or satisfactory alternative therapy options are available.
Pregnancy Category
A Adequate and well-controlled studies have failed to demonstrate a risk to the fetus in the first trimester of pregnancy (and there is no evidence of risk in later trimesters).
B Animal reproduction studies have failed to demonstrate a risk to the fetus and there are no adequate and well-controlled studies in pregnant women.
C Animal reproduction studies have shown an adverse effect on the fetus and there are no adequate and well-controlled studies in humans, but potential benefits may warrant use in pregnant women despite potential risks.
D There is positive evidence of human fetal risk based on adverse reaction data from investigational or marketing experience or studies in humans, but potential benefits may warrant use in pregnant women despite potential risks.
X Studies in animals or humans have demonstrated fetal abnormalities and/or there is positive evidence of human fetal risk based on adverse reaction data from investigational or marketing experience, and the risks involved in use in pregnant women clearly outweigh potential benefits.
N FDA has not classified the drug.
Controlled Substances Act (CSA) Schedule
M The drug has multiple schedules. The schedule may depend on the exact dosage form or strength of the medication.
U CSA Schedule is unknown.
N Is not subject to the Controlled Substances Act.
1 Has a high potential for abuse. Has no currently accepted medical use in treatment in the United States. There is a lack of accepted safety for use under medical supervision.
2 Has a high potential for abuse. Has a currently accepted medical use in treatment in the United States or a currently accepted medical use with severe restrictions. Abuse may lead to severe psychological or physical dependence.
3 Has a potential for abuse less than those in schedules 1 and 2. Has a currently accepted medical use in treatment in the United States. Abuse may lead to moderate or low physical dependence or high psychological dependence.
4 Has a low potential for abuse relative to those in schedule 3. It has a currently accepted medical use in treatment in the United States. Abuse may lead to limited physical dependence or psychological dependence relative to those in schedule 3.
5 Has a low potential for abuse relative to those in schedule 4. Has a currently accepted medical use in treatment in the United States. Abuse may lead to limited physical dependence or psychological dependence relative to those in schedule 4.
Alcohol
X Interacts with Alcohol.

Further information

Always consult your healthcare provider to ensure the information displayed on this page applies to your personal circumstances.