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uroporphyrinogen decarboxylase

 

Definition: an enzyme that participates in heme biosynthesis; it catalyzes the decarboxylation of uroporphyrin III to produce coproporphyrinogen III; it also acts on uroporphyrin I; a deficiency of this enzyme will result in either porphyria cutanea tarda or hepatoerythropoietic porphyria.

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© Copyright 2018 Wolters Kluwer. All Rights Reserved. Review date: Sep 19, 2016.

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