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Medical Term:

ß-hydroxypropionic aciduria

Pronunciation: hi-drok'se-pro'pe-on'ik as'i-dyu're-a

Definition: Elevated levels of ß-hydroxypropionic acid in the urine; seen in defects in methylmalonic acid and propionate metabolism, as well as in ketotic hyperglycinemia syndrome.

© Copyright 2016 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.
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