Skip to Content
Medical Term:

protoporphyrinogen type III oxidase


a mitochondrial enzyme that uses O2 to convert protoporphyrinogen type III to protoporphyrin type III in heme biosynthesis; a deficiency of this enzyme is associated with variegate porphyria.

© Copyright 2017 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.