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Medical Term:

oasthouse urine disease


an autosomal recessively inherited metabolic defect in the absorption of methionine that is converted by intestinal bacteria to a-hydroxybutyric acid; characterized by diarrhea, tachypnea, and marked urinary excretion of a-hydroxybutyric acid (causing an odor like that of an oasthouse).

[oast, kiln for drying hops, malt, or tobacco]

© Copyright 2017 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.