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Medical Term:

melanotic neuroectodermal tumor of infancy


Definition: a benign neoplasm of neuroectodermal origin that most often involves the anterior maxilla of infants in the first year of life. It presents clinically as a rapidly growing blue-black lesion producing a destructive radiolucency; histologically, it is characterized by small, round, undifferentiated tumor cells interspersed with larger polyhedral melanin-producing cells arranged in an alveolar configuration.

Synonym(s): melanoameloblastoma, pigmented ameloblastoma, pigmented epulis, progonoma of jaw, retinal anlage tumor

© Copyright 2016 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.