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Medical Term:

idiopathic pulmonary hemosiderosis

 

Definition: a rare, generally fatal disease of unknown cause, typically affecting small children; characterized by infiltration of pulmonary alveoli with hemosiderin-containing macrophages progressing to diffuse pulmonary fibrosis. Clinical features include recurrent pulmonary hemorrhages, anemia, dyspnea, and cardiorespiratory failure.

Synonym(s): Ceelen-Gellerstedt syndrome

© Copyright 2016 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.
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