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cystathionine ß-synthase

Pronunciation: sis'ta-thi'o-nen sin'thas

Definition: An enzyme catalyzing the reversible hydrolysis of l-cystathionine to l-serine and l-homocysteine. A step in cysteine biosynthesis and in methionine catabolism. A deficiency of this enzyme leads to vascular thrombosis, dislocation of ocular lens, and abnormal development.

Synonym(s): ß-thionase, cysteine synthase, serine sulfhydrase

See Also: cystathionine ?-synthase

Further information

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© Copyright 2018 Wolters Kluwer. All Rights Reserved. Review date: Sep 19, 2016.