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Medical Term:

coproporphyrinogen oxidase


Definition: an enzyme that catalyzes a step in porphyrin biosynthesis, reacting coproporphyrinogen III and O2 to form protoporphyrinogen IX and 2CO2. A deficiency of this enzyme will result in hereditary coproporphyria.

© Copyright 2016 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.