Skip to Content

bullous congenital ichthyosiform erythroderma


Definition: diffusely red, eroded skin at birth, with subsequent scaling, tending to improve in later life, characterized by generalized epidermolytic hyperkeratosis and autosomal dominant inheritance.

Synonym(s): generalized epidermolytic hyperkeratosis, ichthyismus hystrix, ichthyosis hystrix

See Also: epidermolytic hyperkeratosis

Disclaimer: This site is designed to offer information for general educational purposes only. The health information furnished on this site and the interactive responses are not intended to be professional advice and are not intended to replace personal consultation with a qualified physician, pharmacist, or other healthcare professional. You must always seek the advice of a professional for questions related to a disease, disease symptoms, and appropriate therapeutic treatments.
© Copyright 2017 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.