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bullous congenital ichthyosiform erythroderma


Definition: diffusely red, eroded skin at birth, with subsequent scaling, tending to improve in later life, characterized by generalized epidermolytic hyperkeratosis and autosomal dominant inheritance.

Synonym(s): generalized epidermolytic hyperkeratosis, ichthyismus hystrix, ichthyosis hystrix

See Also: epidermolytic hyperkeratosis

Further information

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© Copyright 2018 Wolters Kluwer. All Rights Reserved. Review date: Sep 19, 2016.