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Medical Term:

ATP:cobalamin adenosyltransferase


an enzyme that catalyzes the reaction of ATP, water, and cobalamin to form orthophosphate, pyrophosphate, and adenosylcobalamin. Adenosylcobalamin is required by methylmalonyl-CoA mutase. A deficiency of ATP:cobalamin adenosyltransferase leads to methylmalonic acidemia.

© Copyright 2017 Wolters Kluwer. All Rights Reserved. Review Date: Sep 19, 2016.