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aminoadipic ΄-semialdehyde synthase

Pronunciation: ă-mē′nō-ă-dip′ik se′mē-al′di-hīd sin′thās

Definition: A bifunctional enzyme used in lysine degradation; it has a lysine:α-ketoglutarate reductase activity as well as a saccharopine dehydrogenase activity. A deficiency of this enzyme results in familial hyperlysinemia.

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© Copyright 2018 Wolters Kluwer. All Rights Reserved. Review date: Sep 19, 2016.