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1-phosphofructokinase

Pronunciation: fos'fo-fruk'to-ki'nas

Definition: an enzyme catalyzing phosphorylation of d-fructose 1-phosphate by ATP (or other NTP) to d-fructose 1,6-bisphosphate and ADP (or other NDP); a key step in the metabolism of d-fructose; a deficiency of the muscle enzyme can result in glycogen storage disease type VII.

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© Copyright 2018 Wolters Kluwer. All Rights Reserved. Review date: Sep 19, 2016.

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