Skip to Content


Pronunciation: fos'fo-fruk'to-ki'nas

Definition: an enzyme catalyzing phosphorylation of d-fructose 1-phosphate by ATP (or other NTP) to d-fructose 1,6-bisphosphate and ADP (or other NDP); a key step in the metabolism of d-fructose; a deficiency of the muscle enzyme can result in glycogen storage disease type VII.

Further information

Always consult your healthcare provider to ensure the information displayed on this page applies to your personal circumstances.

© Copyright 2018 Wolters Kluwer. All Rights Reserved. Review date: Sep 19, 2016.