Naegeli syndrome
Pronunciation: nā′gĕ-lē
Definition: reticular skin pigmentation, diminished sweating, hypodontia, hyperkeratosis of the palms and soles, and blistering; may be confused with incontinentia pigmenti but is as common in males as in females; autosomal dominant inheritance.
Synonym(s): Franceschetti-Jadassohn syndrome
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