gangliosidosis
Pronunciation: gang′glē-ō-si-dō′sis
Definition: Any disease characterized, in part, by the abnormal accumulation within the nervous system of specific gangliosides, GM2 gangliosidosis, Tay-Sachs disease; caused by hexosaminidase A enzyme deficiency with accumulation of GM2 ganglioside.
Synonym(s): gangliosialidosis, ganglioside lipidosis
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Examples: glitazone, GI cocktail, etc.
