fumarylacetoacetate hydrolase
Definition: an enzyme that catalyzes the hydrolysis of fumarylacetoacetate to fumarate and acetoacetate; a deficiency indicates tyrosinemia IA.
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Examples: glitazone, GI cocktail, etc.
Definition: an enzyme that catalyzes the hydrolysis of fumarylacetoacetate to fumarate and acetoacetate; a deficiency indicates tyrosinemia IA.
Examples: glitazone, GI cocktail, etc.