Medical Term:

dihydropteridine reductase

Pronunciation: dī-hī-drō-ter′i-dēn rē-dŭk′tās

Definition: An enzyme that catalyzes the reversible formation of tetrahydrobiopterin from dihydrobiopterine using NADPH; a deficiency of this enzyme can result in malignant hyperphenylalaninemia.

Synonym(s): dihydrobiopterin reductase

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Examples: glitazone, GI cocktail, etc.

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