dihydropteridine reductase
Pronunciation: dī-hī-drō-ter′i-dēn rē-dŭk′tās
Definition: An enzyme that catalyzes the reversible formation of tetrahydrobiopterin from dihydrobiopterine using NADPH; a deficiency of this enzyme can result in malignant hyperphenylalaninemia.
Synonym(s): dihydrobiopterin reductase
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Examples: glitazone, GI cocktail, etc.

